Pierre robin sequence in a neonate with suckling difficulty and weight loss.

Role of SOX9 in the Etiology of Pierre-Robin Syndrome

Objective(s:Cleft lip/palate are common congenital anomalies, affecting approximately 2/1000 live births. Pierre Robin Sequence is a subgroup of the cleft palate population. Chromosomal abnormalities near the SOX9 gene disrupt the regulation of this gene and prevent the SOX9 protein from properly controlling the development of facial structures, which leads to isolated PRS. The present study wa...

اانجام بیهوشی عمومی برای خدمات دندانپزشکی یک بیمار مبتلا به Pierre Robin Sequence: گزارش مورد

مقدمه:Pierre Robin Sequence که قبلاً به عنوان سندروم پیر روبین نامیده می‏شد، شامل سه ناهنجاری مادرزادی ماندیبول کوچک، عقب افتادگی زبان و شکاف کام می‏باشد. به طوری که نقص اولیه عامل ایجاد نقص بعدی است. نوزادان مبتلا به این بیماری با مشکلات انسداد راه هوایی، بازگشت محتویات معده به مری وتغذیه همراهند. مداخلات صورت گرفته اغلب جهت حفظ یک راه هوایی باز است. شرح مورد: یکی از مشکلات اصلی با توجه به کو...

سندرم پیرروبین ( THE PIERRE ROBIN SYNDROME )

Tongue-lip adhesion in the management of Pierre Robin sequence with airway obstruction: technique and outcome.

BACKGROUND Airway obstruction and feeding difficulty can occur in patients born with Pierre Robin sequence. In select patients with pronounced micrognathia, surgical intervention to relieve the airway obstruction is necessary. The surgical indications and appropriate surgical procedure continue to have a great deal of controversy. The purpose of this study was to evaluate our experience of tong...

The air-Q intubating laryngeal airway in neonates with difficult airways.

1 Parameswari A, Vakamudi M, Manickam A et al. Nasal fiberoptic–guided oral tracheal intubation in neonates and infants with Pierre Robin sequence. Pediatr Anesth 2011; 21: 170–171. 2 Xue FS, Luo MP. Management of difficult pediatric airways. In: Xue FS, eds. Modern Airway Management: A Key Technique for Clinical Anesthesia and Critical Care Medicine. Zheng-Zhou: Zheng-Zhou University Publishin...